Journal of Rare Cardiovascular Diseases

Budd‑Chiari syndrome (BCS) is a rare clinical disorder which is caused by obstruction of the major hepatic veins or suprahepatic portion of the inferior vena cava. Either thrombosis or a mechanical venous obstruction may be present. BCS has been shown to be associated with a number of diseases including polycythaemia vera, myeloproliferative disorders, malignancy or congenital web of the gastro‑intestinal tract. Right‑sided cardiac tumours, although rarely reported as a cause for BCS, are generally considered as a surgically curable cause for this otherwise potentially lethal clinical condition. JRCD 2018; 3 (6): 219–221.

rare disease; cardiac tumour, cardiac magnetic resonance imaging; computed tomography; echocardiography; cardiac surgery

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