45‑year‑old man with hypertrophic cardiomyopathy after alcohol ablation, progression to dilated cardiomyopathy (RCD code: III‑1B.8a)

Sylwia Wiśniowska‑Śmiałek, Paweł Rubiś, Barbara Biernacka‑Fiałkowska, Marcin Kunecki, Marta Hlawaty, Agata Leśniak‑Sobelga, Magdalena Kostkiewicz, Piotr Podolec

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Abstract


Hypertrophic cardiomyopathy (HCM) is the most common inheritable cardiac disorder with an estimated prevalence of 1:500 in the general population. In minority of patients, with the prevalence approximately of 3–5%, HCM progresses into dilated, end-stage or burn-out phase, characterized by LV wall thinning, systolic dysfunction and LV cavity dilatation. We present a case of a 45 year-old man with endstage HCM with postcapillary pulmonary hypertension, who was experimentally treated with sildenafil. It resulted in noticeable clinical and haemodynamical improvement. JRCD 2014; 2 (1): 23–26

Keywords


cardiomyopathy; sildenafil; end-stage

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DOI: http://dx.doi.org/10.20418%2Fjrcd.vol2no1.157

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