Journal of Rare Cardiovascular Diseases

Aortic stenosis is the most common form of congenital left ventricle outflow tract obstruction. It may be a life threatening ductal-dependent condition in newborns and necessitating urgent percutaneous balloon aortic valvuloplasty (BAV). Although early results of valvuloplasty are usually satisfactory, long-term follow-up show frequent incidence of gradually progressing aortic insufficiency that requires valve replacement surgery. The case report presented below concerns a young patient with a history of BAV in childhood who developed severe aortic regurgitation accompanied by combined post- and pre-capillary pulmonary hypertension.

aortic valve replacement; bioprosthesis; echocardiograph;, heart catheterization; iliac artery occlusion; congestive heart failure; sildenafil

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