Pregnant woman with Ebstein’s anomaly

Agata Leśniak‑Sobelga, Lidia Tomkiewicz‑Pająk, Jacek Pająk, Piotr Podolec

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A 34-year-old female with Ebstein’s anomaly presented to our centre at 19th week of her fi rst pregnancy with a history of dyspnea, palpitations and syncopes. Echocardiogram showed typical signs of Ebstein’s anomaly with severe tricuspid regurgitation, large atrial septal defect with left-to-right shunt and elevated right ventricular systolic pressure. She was prescribed metoprolol and anticoagulation with low-molecular-weight heparin. The pregnancy course was uneventful. She delivered by vaginal route in 36th week of pregnancy a healthy male baby weighing 2140 g. On the 6th day after delivery she experienced tachycardia, dyspnea, dizziness. Clinical examination and additional studies revealed only slight limb oedema
and low haemoglobin level. After treatment with furosemide and prescription of folic acid and iron supplementation she was discharged home in a good clinical condition after 4 days. JRCD 2012; 1: 13–17

Key words: Tricuspid valve regurgitation; Atrial septal defect; Pulmonary hypertension


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