Case report on aortic valve replacement in adult woman with systemic mastocytosis (RCD code: VIII)
We present a case of a 50 year-old woman who was referred to our department with severe symptomatic aortic stenosis and systemic mastocytosis. Conventional mechanical aortic valve replacement was performed successfully with the use of perioperative protocol based on dexamethasone, cetirizine and ranitidine. The only postoperative event was an onset of atrial fibrillation which was treated with amiodarone infusion. 8 days after surgery the patient was discharged home. JRCD 2017; 3 (2): 54–55
Valent P, Horny HP, Escribano L. Diagnostic criteria and classification of mastocytosis: a consensus proposal. Conference report of Year 2000 Working Conference on Mastocytosis. Leuk Res 2001; 25: 603–625.
Valent P, Akin C, Arock M. Definitions, criteria and global classification of mast cell disorders with special reference to mast cell activation syndromes: a consensus proposal. Int Arch Allergy Immunol 2012; 157: 215–225.
Valent P, Akin C, Escribano L. Standards and standardization in mastocytosis: consensus statements on diagnostics, treatment recommendations and response criteria. Eur J Clin Invest 2007; 37: 435–453.
Dewachter P, Castells MC, Hepner DL. Perioperative Management of Patients with Mastocytosis. Anesthesiology 2014; 120; 753–759.
Corral‑Velez V, Lopez‑Delgado JC, Betancur‑Zambrano NL. The inflammatory response in cardiac surgery: an overview of the pathophysiology and clinical implications. Inflamm Allergy Drug Targets 2015; 13: 367–370.
Wanamaker KM, Magovern GJ Jr, Moraca RJ. Aortic valve replacement in patients with systemic mastocytosis. J Card Surg 2012; 27: 189–191.
Duggal N, Payne E, Engoren M. Aneurysm Repair in a Patient With Systemic Mastocytosis. J Cardiothorac Vasc Anesth 2015; 29: 1025–1028.
Moro JA, Almenar L, Jarque I. Heart transplantation in a patient with systemic mastocytosis., J Heart Lung Transplant 2008; 27: 689–691.
Damodar S, John CN, Gopalakrishnan G. Mast cell disease: surgical and anesthetic implications. J Pediatr Hematol Oncol 2006; 28: 446–449.
Lee S, Hess EP, Nestler DM. Antihypertensive medication use is associated with increased organ system involvement and hospitalization in emergency department patients with anaphylaxis. J Allergy Clin Immunol 2013; 131: 1103–1108.
Mueller UR, Haeberli G. Use of beta‑blockers during immunotherapy for Hymenoptera venom allergy. J Allergy Clin Immunol 2005; 115: 606–610.
Tunon‑de‑Lara J, Villanueva P, Marcos M. ACE inhibitors and anaphylactic reactions during venom immunotherapy. Lancet 1992; 340: 908.
Simons FE, Ardusso LR, Bilò MB. World allergy organization guidelines for the assessment and management of anaphylaxis. World Allergy Organ J 2011; 4: 13–37.
Brockow K, Bonadonna P. Drug allergy in mast cell disease. Curr Opin Allergy Clin Immunol 2012; 12: 354–360.
Desborough JP, Taylor I, Hattersley A, et al. Massive histamine release in a patient with systemic mastocytosis. Br J Anaesth 1990; 65: 833–836.
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