Pulmonary arterial hypertension; time is crucial for survival. A case report of late diagnosis in a real life scenario.

Maryla Mianowana, Łukasz Siudak, Piotr Błaszczak


Pulmonary arterial hypertension is a rare disease of pulmonary circulation with poor prognosis if left untreated or diagnosed with a delay. Active screening for the disease is non-effective in general population but there are populations of increased risk in whom all the efforts should be taken to establish the diagnosis early. We present two cases of late diagnosis despite clear clinical picture in one and at-risk population in another case with treatment administration to late to obtain satisfactory results. We discuss pitfalls and delays that finally resulted in treatment failure.


pulminary hypertension, differential diagnosis, delay, prognosis


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DOI: http://dx.doi.org/10.20418%2Fjrcd.vol4no3.389


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