An Extremely Rare Congenital Association: Uni- cuspid Aortic Valve with Left Ventricular Noncom- paction (RCD code: III-5A.1.o)

Souzan Tatari

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Abstract


Unicuspid aortic valve is a rare congenital abnormality with a prevalence of 0.02% in the adult population. Left ventricular noncompaction is another congenital anomaly with an incidence of 0.05%. Unicuspid aortic valve with severe aortic regurgitation and left ventricular
noncompaction was found in a 15-year-old deaf male patient who presented with shortness of breath, orthopnoea and intermittent palpitations. JRCD 2019; 4 (4): xx–xx


Keywords


rare disease; congenital heart disease; echocardiography; magnetic resonance imaging

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DOI: http://dx.doi.org/10.20418%2Fjrcd.vol4no3.390

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