Pregnancy in patient with Turner syndrome, after surgery for coarctation of the aorta, with bicuspid aortic valve and ascending aortic aneurysm (RCD code: VII-I-1B.6)

Lidia Tomkiewicz-Pająk, Agata Leśniak-Sobelga, Krzysztof Rytlewski, Tomasz Pawelec, Bogdan Kapelak, Agnieszka Żygadło, Maria Olszowska, Piotr Podolec

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Abstract


A 30‑year‑old woman with Turner Syndrome was admitted to our centre in 12th week of her first pregnancy with a history o surgical correction of coarctation of aorta. She was asymptomatic with good general condition. Transthoracic echocardiography revealed a bicuspid aortic valve with moderate regurgitation and an ascending aorta aneurysm. In angio‑MR the narrowing of the isthmus of the aorta over 50% was seen with peak systolic gradient found in echocardiography approximately 41 mmHg. She was prescribed metoprolol and was closely monitored, the course of pregnancy was uneventful. In 24th week of pregnancy steroids were administered as a preparation for earlier delivery. She delivered in 34th week of pregnancy a healthy baby weighting 2100 grams. Caesarean section was performed in the cardiothoracic surgery ward and after delivery she underwent percutaneous angioplasty of coarctation of aorta with stent implantation. Six weeks after labour she underwent the Bental de Bono procedure with artificial aortic valve implantation. In six‑month observation patient was in good general condition, echocardiography showed normal ascending aorta diameter. JRCD 2013; 1 (4): 16–20


Keywords


Pregnancy in patient with Turner syndrome, coarctation of aorta

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DOI: http://dx.doi.org/10.20418%2Fjrcd.vol1no4.58

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Journal of Rare Cardiovascular Diseases (JRCD)
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