Adult patient with truncus arteriosus type I. Management and follow‑up (RCD code: IV‑1C.3b)

Jakub Stępniewski, Monika Komar, Piotr Wilkołek, Bartosz Sobień, Anna Tyrka, Barbara Widlińska, Lidia Tomkiewicz‑Pająk, Piotr Podolec

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Abstract


Truncus arteriosus is a congenital heart malformation where systemic, pulmonary and coronary circulation is supplied by a single artery arising from the heart. Surgical correction of  this disorder remains the treatment of choice. Presenting the case of a 21-year-old male, who underwent surgical correction of the anomaly in youth, we review management and follow-up strategy for adult patients after correction of truncus arteriosus. Conduit failure is the most commonly observed long-term consequence of the surgical correction. We evaluate diagnostic algorithm and  indications for conduit replacement. JRCD 2014; 1 (8): 15–18

Keywords


grown-up congenital heart disease, single arterial trunk, ventricular septal defect, conduit

References


Moller JH. Prevalence and incidence of cardiac malformations In: Moller JH, editor. Surgery of congenital heart disease, Pediatric Cardiac Care Consortium 1984–1995. Philadelphia: Futura; 1998: 19–26.

Mavroudis C, Backer CL. Truncus arteriosus. In: Mavroudis C, Backer CL, editors. Pediatric cardiac surgery. 3rd ed. St Louis: CV Mosby; 2003: 339–352.

Klewer SE, Behrendt DM, Atkins DL. Truncus arteriosusIn: Moller JH, editor. Surgery of congenital heart disease, Pediatric Cardiac Care Consortium 1984–1995. Philadelphia: Futura; 1998: 271–285.

Corno AF. Congenital heart defects. Decision making for surgery. Vol 2. Darmstadt, Germany: Steinkopf Verlag; 2004: 71–81.

Bove EL, Lupinetti FM, Pridjian AK, et al. Results of a policy of primary repair of truncus arteriosus in the neonate J Thorac Cardiovasc Surg 1993; 105: 1057–1066.

Collett RW, Edwards JE. Persistent truncus arteriosus; a classification according to anatomic types. Surg Clin North Am. 1949; 29: 1245–1270.

Van Praagh R, Van Praagh S. The anatomy of common aorticopulmonary trunk (truncus arteriosus communis) and its embryologic implications. A study of 57 necropsy cases. Am J Cardiol. 1965; 16: 406–425.

Hanley FL, Heinemann MK, Jonas RA, et al. Repair of truncus arteriosus in the neonate J Thorac Cardiovasc Surg 1993; 105: 1047–1056.

Jahangiri M, Zurakowski D, Mayer JE, et al. Repair of the truncal valve and associated interrupted arch in neonates with truncus arteriosus J Thorac Cardiovasc Surg 2000; 119: 508–514.

Thompson LD, McElhinney DB, Reddy VM, et al. Neonatal repair of truncus arteriosus: continuing improvement in outcomes Ann Thorac Surg 2001; 72: 391–395.

Brizard CP, Cochrane A, Austin C, et al. Management strategy and long-term outcome for truncus arteriosus Eur J Cardiothorac Surg 1997; 11: 687–696.

Brown JW, Ruzmetov M, Okada Y, et al. Truncus arteriosus repair: outcomes, risk factors, reoperation and management Eur J Cardiothorac Surg 2001; 20: 221–227.

Ullmann MV, Gorenflo M, Sebening C, et al. Long-term results after repair of truncus arteriosus communis in neonates and infants Thorac Cardiovasc Surg 2003; 51: 175–179.

Dearani JA, Danielson GK, Puga FJ, et al. Late follow-up of 1095 patients undergoing operation for complex congenital heart disease utilizing pulmonary ventricle to pulmonary artery conduits Ann Thorac Surg 2003; 75: 399–410.




DOI: http://dx.doi.org/10.20418%2Fjrcd.vol1no8.66

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Journal of Rare Cardiovascular Diseases (JRCD)
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