Journal of Rare Cardiovascular Diseases

Truncus arteriosus is a congenital heart malformation where systemic, pulmonary and coronary circulation is supplied by a single artery arising from the heart. Surgical correction of  this disorder remains the treatment of choice. Presenting the case of a 21-year-old male, who underwent surgical correction of the anomaly in youth, we review management and follow-up strategy for adult patients after correction of truncus arteriosus. Conduit failure is the most commonly observed long-term consequence of the surgical correction. We evaluate diagnostic algorithm and  indications for conduit replacement. JRCD 2014; 1 (8): 15–18

grown-up congenital heart disease, single arterial trunk, ventricular septal defect, conduit

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