Pregnant woman with Eisenmenger’s syndrome (RCD code: VII-II-1A.4d)

Grzegorz Kopeć, Agata Leśniak-Sobelga, Magdalena Kaźnica-Wiatr, Anna Tyrka, Marcin Waligóra, Krzysztof Rytlewski, Piotr Podolec

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Pregnancy in women with pulmonary arterial hypertension due to congenital heart disease is associated with significant morbidity and mortality both in the mother and fetus. We report a case of a 25-year-old woman with Eisenmenger’s syndrome who got pregnant when treated with bosentan. Bosentan was changed to sildenafil. During the course of pregnancy she developed ischemic stroke. She delivered in the 33 week of gestation. We present our treatment approach and review the current literature on pregnany in pulmonary arterial hypertension. JRCD 2013; 1 (3): 27–31


pulmonary hypertension; congenital heart disease; pregnancy


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