Pulmonary arterial hypertension after systemic‑to‑pulmonary shunt correction (RCD code: II-1A.4d)

Magdalena Kaznica-Wiatr, Grzegorz Kopeć, Piotr Podolec

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Pulmonary arterial hypertension develops in a significant number of patients with congenital heart diseases. Congenital heart diseases predispose to pulmonary vascular remodeling as a result of increased pulmonary blood flow and increased pulmonary pressure. Pulmonary arterial hypertension associated with congenital heart diseases is a major determinant of functional capacity and survival in this group of patients. JRCD 2013; 1 (3): 32–35


congenital heart disease; pulmonary hypertension; Endothelin Receptor Antagonist


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DOI: http://dx.doi.org/10.20418%2Fjrcd.vol1no3.91


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