Pulmonary arterial hypertension after systemic‑to‑pulmonary shunt correction (RCD code: II-1A.4d)
Full Text:
Abstract
Pulmonary arterial hypertension develops in a significant number of patients with congenital heart diseases. Congenital heart diseases predispose to pulmonary vascular remodeling as a result of increased pulmonary blood flow and increased pulmonary pressure. Pulmonary arterial hypertension associated with congenital heart diseases is a major determinant of functional capacity and survival in this group of patients. JRCD 2013; 1 (3): 32–35
Keywords
References
Galie N, Manes A, Palazzini M, et al. Management of pulmonary arterial hypertension associated with congenital systemic‑to‑pulmonary shunts and Eisenmenger’s syndrome. Drugs 2008; 68: 1049–1066.
Humbert M, Sitbon O, Chaouat A, et al. Pulmonary arterial hypertension in France: results from a national registry. Am J Respir Crit Care Med 2006; 173: 1023–1030.
Duffels MG, Engelfriet PM, Berger RM, et al. Pulmonary arterial hypertension in congenital heart disease: an epidemiologic perspective from a Dutch registry. Int J Cardiol 2007; 120: 198–204.
Marelli AJ, Mackie AS, Ionescu‑Ittu R, et al. Congenital heart disease in the general population: changing prevalence and age distribution. Circulation 2007; 115: 163–172.
Galie N, Hoeper M, Humbert M. Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Heart J 2009; 30: 2493–2537.
Diller GP, Gatzoulis MA. Pulmonary vascular disease in adults with congenital heart disease. Circulation 2007; 115: 1039–1050.
Beghetti M, Galie N. Eisenmenger syndrome a clinical perspective in a new therapeutic era of pulmonary arterial hypertension. J Am Coll Cardiol 2009; 53: 733–740.
Beghetti M, Barst R, Naeije R. Pulmonary arterial hypertension related to congenital heart disease. Elsevier GmbH 2006
Dimopoulos K, Giannakoulas G, Wort SJ, et al. Pulmonary arterial hypertension in adults with congenital heart disease: distinct differences from other causes of pulmonary arterial hypertension and management implications. Curr Opin Cardiol 2008; 23: 545–554.
DOI: http://dx.doi.org/10.20418%2Fjrcd.vol1no3.91
Refbacks
- There are currently no refbacks.