Journal of Rare Cardiovascular Diseases

ISSN: 2299-3711 (Print) e-ISSN: 2300-5505 (Online)

Matusik

Exercise ECG unmasked Brugada sign: manifestation of the risk of sports‑associated sudden cardiac arrest (RCD code: V‑1A.1) Matusik PT, Komar M, Podolec J, Karkowski G, Lelakowski J, Podolec P Full Text: PDF Abstract Sports‑associated sudden cardiac arrest (SCA) constitutes an important problem. Causes of SCA during sport activities include Brugada syndrome (BrS) among others. We […]

Majewski

Broad QRS complex tachycardia in a patient with myotonic dystrophy (Steinert disease) (RCD code: V‑4O) Jacek Majewski, Jacek Lelakowski Full Text: PDF Abstract Myotonic dystrophy is a rare inherited condition affecting primarily skeletal muscles and commonly associated with cardiovascular pathology. We report a case of a 50- year old female with myotonic dystrophy type 1 […]

Barabash

Coronary sinus atrial septal defect in adult (RCD code: IV‑2B.1) Oksana Barabash, Yuriy Ivaniv, Ihor Ivaniv, Oksana Predzemirska Full Text: PDF Abstract We present a case report of a 45‑year old man, who was admitted to medical center due to dyspnea and cough. Right bundle branch block was detected on electrocardiography. Transthoracic echocardiography demonstrated coronary […]

Błaut-Jurkowska

Electrocardiographic abnormalities in patients with pulmonary sarcoidosis (RCD code: III) Justyna Błaut-Jurkowska, Magdalena Kaźnica-Wiatr, Agnieszka Żygadło, Lidia Tomkiewicz-Pająk, Piotr Podolec, Maria Olszowska Full Text: PDF Abstract Sarcoidosis is a systemic inflammatory disease characterized by the presence of noncaseating granulomas. Etiology of the disease remains unknown. From 3.7% to 54.9% patients with extra‑cardiac sarcoidosis have asymptomatic […]

Matusik

Brugada syndrome: current diagnostics, epidemiology, genetic data and novel mechanisms (RCD code: V‑1A.1) Paweł Tomasz Matusik, Joanna Pudło, Anna Rydlewska, Jakub Podolec, Jacek Lelakowski, Piotr Podolec Full Text: PDF Abstract Brugada syndrome (BrS) is a cardiac channelopathy associated with ventricular arrhythmias and sudden cardiac death. Diagnosis of BrS is based on type 1 BrS electrocardiogram […]

Podolec

“Let (the hospital) serve!”. Pope John Paul II. Visit at the John Paul II Hospital in Krakow, 9 June 1997 Piotr Podolec Full Text: PDF Abstract This June, here in Krakow we witness two important anniversaries. First, our hospital, now called after Pope John Paul II, is already 100 years old. Secondly, 20 years have […]

Hussain

An uncommon cause of right heart failure: primary cardiac pre-B cell acute lymphoblastic leukemia (RCD code: VI-2C.1). Bilal Hussain, Fateh Ali Tipoo Sultan, Farouk Mookadam Full Text: PDF Abstract Hematological malignancies are protean in their presentations. Primary cardiac tumors are exceedingly rare, and primary cardiac leukemia presenting as an isolated mass is even rare. Here, […]

Wiśniowska‑Śmiałek

Hemangioma of the left ventricle (RCD code: VI-1B.4) Sylwia Wiśniowska‑Śmiałek, Paweł Rubiś, Katarzyna Holcman, Tomasz Myrdko, Magdalena Kostkiewicz, Małgorzata Urbańczyk‑Zawadzka, Bogusław Kapelak, Piotr Podolec Full Text: PDF Abstract Cardiac tumors are quite rare, and differential diagnosis of them is challenging.We present the case report of a young man complaining on non specific chest pain who […]

Hussain

A rare cardiac manifestation of Brucellosis (RCD code: VIII) Bilal Hussain, Fateh Ali Tipoo Sultan Full Text: PDF Abstract Brucellosis, a zoonosis caused by gram negative bacillus Brucella, is characterized by a systemic illness with vague symptoms. Though, cardiac involvement with Brucella is reported mostly as endocarditis, the occurrence of exclusive Brucella constrictive pericarditis without […]

Knap

A successful treatment of ischemic cardiomyopathy associated with left ventricular aneurysm and chronic ischaemic mitral regurgitation (RCD code: III-1B.9.o). Klaudia Knap, Leszek Drabik, Justyna Błaut-Jurkowska, Michał Pacia, Maciej Krupińsk, Małgorzata Urbańczyk-Zawadzka, Wojciech Płazak Full Text: PDF Abstract Complications of myocardial infarction (MI) such as left ventricular aneurysm, chronic ischaemic mitral regurgitation (CIMR) and heart failure […]